jobs syndrome - Medical Dictionary

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jobs syndrome		A disorder of neutrophils characterized by the presence of abnormal or absent chemotactic responses and hyperimmunoglobulinemia E. It is transmitted as an autosomal recessive trait and most cases reported have been in girls. [ Articles \| Books \| Images \| Discussion groups ]

Additional comments : (Hyper-IgE Syndrome, Hyperimmunoglobulin E-Recurrent Infection Syndrome) Articles Childhood bullous pemphigoid in association with hyperimmunoglobulin E syndrome. Authors: Erbagci Z Journal: Pediatr Dermatol Congenital immunodeficiency disorder. Authors: Abhilash N, Radhakrishnan S, Arun MV, Sasidharan PK Journal: J Assoc Physicians India Dental observations of hyper IgE disorder. Authors: Aldous JA, Olson GJ, Parkin MJ Journal: J Clin Pediatr Dent Destructive staphylococcal pleuropneumonia in a two-year-old boy with hyperimmunoglobulin-E syndrome. Authors: Tomi? J, Odri I, Pasi? S, Jovanovi? M Journal: Med Pregl Methicillin-resistant Staphylococcus aureus (MRSA) mitral valve acute bacterial endocarditis (ABE) in a patient with Job's syndrome (hyperimmunoglobulin E syndrome) successfully treated with linezolid and high-dose daptomycin. Authors: Cunha BA, Krol V, Kodali V Journal: Heart Lung The hyper-IgE syndrome is not caused by a microdeletion syndrome. Authors: Pfeifer D, Woellner C, Petersen A, Pietrogrande MC, Franco JL, Yeganeh M, Ehl S, Matamoros N, Sprecher E, Puck JM, Veelken H, Grimbacher B Journal: Immunogenetics Hyperimmunoglobulin E syndrome and tyrosine kinase 2 deficiency. Authors: Minegishi Y, Karasuyama H Journal: Curr Opin Allergy Clin Immunol [Pneumatocele during long-lasting observation of hyper IgE patient] Authors: Nowicka U, Wiatr E, Kupis W, Burakowska B, Folcik K, Or?owski T, Roszkowski-Sliz K Journal: Pneumonol Alergol Pol STAT3 mutation in the original patient with Job's syndrome. Authors: Renner ED, Torgerson TR, Rylaarsdam S, Añover-Sombke S, Golob K, LaFlam T, Zhu Q, Ochs HD Journal: N Engl J Med STAT3 signaling and the hyper-IgE syndrome. Authors: Levy DE, Loomis CA Journal: N Engl J Med STAT3 mutations in the hyper-IgE syndrome. Authors: Holland SM, DeLeo FR, Elloumi HZ, Hsu AP, Uzel G, Brodsky N, Freeman AF, Demidowich A, Davis J, Turner ML, Anderson VL, Darnell DN, Welch PA, Kuhns DB, Frucht DM, Malech HL, Gallin JI, Kobayashi SD, Whitney AR, Voyich JM, Musser JM, Woellner C, Schäffer AA, Puck JM, Grimbacher B Journal: N Engl J Med Job syndrome masquerading as non-accidental injury. Authors: Walsh J, Reardon W Journal: Arch Dis Child Diffuse large B-cell lymphoma in hyperimmunoglobulinemia E syndrome. Authors: Wallet N, Ghez D, Delarue R, Suarez F, Rubio MT, Fischer A, Canioni D, Varet B, Hermine O Journal: Clin Lymphoma Myeloma Rituximab in a patient with Hyper-IgE syndrome. Authors: Trendelenburg M, Schifferli JA Journal: Arch Dermatol [Pneumocystis carinii pneumonia in a patient with hyper-IgE syndrome] Authors: Kubota M, Takayanagi N, Kurashima K, Miyahara Y, Hara K, Saito H, Tokunaga D, Ubukata M, Yanagisawa T, Sugita Y, Kawabata Y Journal: Nihon Kokyuki Gakkai Zasshi The hyper IgE syndrome and mutations in TYK2. Authors: Woellner C, Schäffer AA, Puck JM, Renner ED, Knebel C, Holland SM, Plebani A, Grimbacher B Journal: Immunity Acquired factor VIII deficiency associated with a novel primary immunodeficiency suggestive of autosomal recessive hyper IgE syndrome. Authors: Ozgur TT, Asal GT, Gurgey A, Tezcan I, Ersoy F, Sanal O Journal: J Pediatr Hematol Oncol A case of hyper-IgE syndrome. Authors: de Alwis AC, de Silva R, Gunawardena S, Weerasuriya DC, Jayaweera AH Journal: Ceylon Med J Brain abnormalities in patients with hyperimmunoglobulin E syndrome. Authors: Freeman AF, Collura-Burke CJ, Patronas NJ, Ilcus LS, Darnell D, Davis J, Puck JM, Holland SM Journal: Pediatrics A young man with hyperimmunoglobulin-E syndrome and IgA and IgG deficiencies. Authors: Fuller K, Pearce A, Raftos J Journal: Clin Exp Dermatol Causes of death in hyper-IgE syndrome. Authors: Freeman AF, Kleiner DE, Nadiminti H, Davis J, Quezado M, Anderson V, Puck JM, Holland SM Journal: J Allergy Clin Immunol Unusual psoriasiform lesions in a patient with Hyper-IgE syndrome. Authors: Li XL, Geng SM, Lei XB, Xiao SX, Liu Y, Peng ZH Journal: J Eur Acad Dermatol Venereol Congenital patent ductus venosus: an association with the hyper IgE syndrome. Authors: Sagiv-Friedgut K, Witzling M, Dalal I, Vinkler C, Someh E, Levine A Journal: J Pediatr Hyper-IgE syndrome associated with an IL-4-producing gamma/delta(+) T-cell clone. Authors: Simon HU, Seger R Journal: J Allergy Clin Immunol A patient with hyper-immunoglobulin E syndrome 25 years later. Authors: Cozzani E, Marro I, Murialdo G, Rebora A, Parodi A Journal: Int J Dermatol Coronary artery aneurysms in patients with hyper IgE recurrent infection syndrome. Authors: Ling JC, Freeman AF, Gharib AM, Arai AE, Lederman RJ, Rosing DR, Holland SM Journal: Clin Immunol Human tyrosine kinase 2 deficiency reveals its requisite roles in multiple cytokine signals involved in innate and acquired immunity. Authors: Minegishi Y, Saito M, Morio T, Watanabe K, Agematsu K, Tsuchiya S, Takada H, Hara T, Kawamura N, Ariga T, Kaneko H, Kondo N, Tsuge I, Yachie A, Sakiyama Y, Iwata T, Bessho F, Ohishi T, Joh K, Imai K, Kogawa K, Shinohara M, Fujieda M, Wakiguchi H, Pasic S, Abinun M, Ochs HD, Renner ED, Jansson A, Belohradsky BH, Metin A, Shimizu N, Mizutani S, Miyawaki T, Nonoyama S, Karasuyama H Journal: Immunity Unusual coexistence of molluscum contagiosum and verruca plana in a hyper-IgE syndrome. Authors: Lei XB, Geng SM, Zeng WH, Tan SS, Wang JM, Xiao SX Journal: Int J Dermatol The clinical and laboratory survey of Iranian patients with hyper-IgE syndrome. Authors: Moin M, Farhoudi A, Movahedi M, Rezaei N, Pourpak Z, Yeganeh M, Gharagozlou M, Mirsaeid Ghazi B, Arshi S, Mansouri D, Sherkat R, Kashef S, Mahmoudi M, Nabavi M, Aghamohammadi A Journal: Scand J Infect Dis Cavitary Legionella pneumonia in a patient with immunodeficiency due to Hyper-IgE syndrome. Authors: Di Stefano F, Verna N, Di Gioacchino M Journal: J Infect Pneumocystis jiroveci infection in patients with hyper-immunoglobulin E syndrome. Authors: Freeman AF, Davis J, Anderson VL, Barson W, Darnell DN, Puck JM, Holland SM Journal: Pediatrics [Multilocular furunculosis and chronic-persisting eczema in a 17-year-old patient] Authors: Göppner D, Hoschna M, Kalinski T, Franke I, Gollnick H, Leverkus M Journal: J Dtsch Dermatol Ges Atopic dermatitis or hyper-IgE syndrome? Authors: Ohameje NU, Loveless JW, Saini SS Journal: Allergy Asthma Proc Hyper-IgE syndrome and autoimmunity in Mexican children. Authors: Yamazaki-Nakashimada M, Zaltzman-Girshevich S, Garcia de la Puente S, De Leon-Bojorge B, Espinosa-Padilla S, Saez-de-Ocariz M, Carrasco-Daza D, Hernandez-Bautista V, Pérez-Fernandez L, Espinosa-Rosales F Journal: Pediatr Nephrol Disseminated white papules. Authors: Yang CH, Lee WI, Hsu TS Journal: Arch Dermatol Hyperimmunoglobulin E syndrome (job syndrome) discovered in a patient following corrective spine surgery: case report and review of the literature. Authors: Tan WM, Kandiah DA, Tan SB Journal: Spine [Jobs syndrome associated with Hodgkins lymphoma] Authors: Fleta-Asín B, Gonzalvo-Liarte C, Palomera-Bernal L, Cía-Gómez P Journal: Med Clin (Barc) Linezolid-resistant Staphylococcus aureus in two pediatric patients receiving low-dose linezolid therapy. Authors: Roberts SM, Freeman AF, Harrington SM, Holland SM, Murray PR, Zelazny AM Journal: Pediatr Infect Dis J Critical aneurysmal dilatation of the thoracic aorta in young adolescents with variant hyperimmunoglobulin E syndrome. Authors: van der meer JW, Weemaes CM, van Krieken JH, Blomjous CE, van Die CE, Netea MG, Bredie SJ Journal: J Intern Med A homozygous missense mutation in PEPD encoding peptidase D causes prolidase deficiency associated with hyper-IgE syndrome. Authors: Hershkovitz T, Hassoun G, Indelman M, Shlush LI, Bergman R, Pollack S, Sprecher E Journal: Clin Exp Dermatol Imaging in hyper-IgE syndrome. Authors: Alkadhi H, Wildermuth S, Russi EW, Marincek B, Boehm T Journal: Respiration Interferon-alpha treatment of molluscum contagiosum in a patient with hyperimmunoglobulin E syndrome. Authors: Kilic SS, Kilicbay F Journal: Pediatrics Peripheral T-cell lymphoma and Job's syndrome: a rare association. Authors: Onal IK, Kurt M, Altundag K, Aksoy S, Dincer M, Gullu I Journal: Med Oncol Hyperimmunoglobulin E syndrome: two cases and a review of the literature. Authors: DeWitt CA, Bishop AB, Buescher LS, Stone SP Journal: J Am Acad Dermatol 2. Update on primary immunodeficiency diseases. Authors: Bonilla FA, Geha RS Journal: J Allergy Clin Immunol Lithium: a potential treatment for hyper-IgE syndrome. Authors: Namazi MR, Handjani F Journal: Med Hypotheses Hyper IgE syndrome: report of two cases with moderate elevation of IgE. Authors: Muhammed K Journal: Indian J Dermatol Venereol Leprol Hodgkin lymphoma developing in a 4.5-year-old girl with hyper-IgE syndrome. Authors: Kashef MA, Kashef S, Handjani F, Karimi M Journal: Pediatr Hematol Oncol Severely impaired IL-12/IL-18/IFNgamma axis in patients with hyper IgE syndrome. Authors: Netea MG, Kullberg BJ, van der Meer JW Journal: Eur J Clin Invest New insights into the pathogenesis of the hyperimmunoglobulinaemia E syndrome. Authors: Sillaber C, Valent P Journal: Eur J Clin Invest Association of hyperimmunoglobulin E syndrome and Gianotti-Crosti syndrome. Authors: Chuh A Journal: Pediatr Infect Dis J Hyper-IgE syndrome with widespread premalign oral papillomas treated with interferon alpha2b. Authors: Ozarma?an G, Didem Yazgano?lu K, Agaçfidan A Journal: Acta Derm Venereol Primary immune deficiencies presenting in adults: seven years of experience from Iran. Authors: Mansouri D, Adimi P, Mirsaedi M, Mansouri N, Tabarsi P, Amiri M, Jamaati HR, Motavasseli M, Baghaii N, Cheraghvandi A, Rouhi R, Roozbahany NA, Zahirifard S, Mohammadi F, Masjedi MR, Velayati AA, Casanova JL, Speert DP, Elwood RK, Schellenberg R, Turvey SE Journal: J Clin Immunol No indication for a defect in toll-like receptor signaling in patients with hyper-IgE syndrome. Authors: Renner ED, Pawlita I, Hoffmann F, Hornung V, Hartl D, Albert M, Jansson A, Endres S, Hartmann G, Belohradsky BH, Rothenfusser S Journal: J Clin Immunol Hyper-IgE syndrome is not associated with defects in several candidate toll-like receptor pathway genes. Authors: Hawn TR, Ozinsky A, Williams LM, Rodrigues S, Clark A, Pham U, Hill HR, Ochs H, Aderem A, Liles WC Journal: Hum Immunol Invasive aspergillosis in primary immunodeficiencies. Authors: Almyroudis NG, Holland SM, Segal BH Journal: Med Mycol Production of biologically active recombinant human soluble CD23 and its effect on PBMCs isolated from hyper-IgE blood. Authors: Daniels BB, Askew SL, van de Venter M, Oosthuizen V Journal: Cell Immunol [Hyper-IgE syndrome] Authors: Joh K Journal: Nippon Rinsho Oral tolerance in the absence of naturally occurring Tregs. Authors: Mucida D, Kutchukhidze N, Erazo A, Russo M, Lafaille JJ, Curotto de Lafaille MA Journal: J Clin Invest Distinct gene expression patterns of peripheral blood cells in hyper-IgE syndrome. Authors: Tanaka T, Takada H, Nomura A, Ohga S, Shibata R, Hara T Journal: Clin Exp Immunol Severe periodontitis in a 5-year-old girl with hyperimmunoglobulin E syndrome. Authors: Tsang P, Derkson G, Priddy R, Junker AK, Slots J, Larjava H Journal: Pediatr Dent Chronic inflammatory demyelinating polyneuropathy in a patient with hyperIgEaemia. Authors: Kimura A, Yoshino H, Yuasa T Journal: J Neurol Sci The dental management of a patient with hyperimmunoglobulinemia E syndrome: a case report. Authors: McAuliffe NJ, Hunter ML, Kau CH, Hunter B, Knox J Journal: Int J Paediatr Dent Hyperimmunoglobulin E syndrome. Authors: Rosenberg BE Journal: Dermatol Online J Cyclosporin A therapy in a case with hyperimmunoglobulin E and nephrotic syndrome. Authors: Bong CN, Huang SC, Wang CL, Liu PM, Chen HH, Yang KD Journal: J Microbiol Immunol Infect [Hyper-IgE syndrome] Authors: Takada H, Nomura A, Hara T Journal: Nihon Rinsho Meneki Gakkai Kaishi Hyper-IgE syndromes. Authors: Grimbacher B, Holland SM, Puck JM Journal: Immunol Rev Recurrent Staphylococcus aureus chalazia in hyperimmunoglobulinemia E (Job's) syndrome. Authors: Destafeno JJ, Kodsi SR, Primack JD Journal: Am J Ophthalmol Non-Hodgkin's lymphoma in Job's syndrome: a case report and literature review. Authors: Leonard GD, Posadas E, Herrmann PC, Anderson VL, Jaffe ES, Holland SM, Wilson WH Journal: Leuk Lymphoma Hyper IgE in New Zealand black mice due to a dominant-negative CD23 mutation. Authors: Lewis G, Rapsomaniki E, Bouriez T, Crockford T, Ferry H, Rigby R, Vyse T, Lambe T, Cornall R Journal: Immunogenetics Cutaneous manifestations of hyper-IgE syndrome in twins: a case report from Saudi Arabia. Authors: Samdani AJ, Tania A Journal: J Pak Med Assoc [Necrotising fasciitis in hyper-IgE syndrome] Authors: Erdos M, Nagy L, Szentkereszty Z, Sáfrány G, Maródi L Journal: Orv Hetil Dermatitis and the newborn rash of hyper-IgE syndrome. Authors: Eberting CL, Davis J, Puck JM, Holland SM, Turner ML Journal: Arch Dermatol A rare cause of gastrointestinal bleeding in a patient with hyper-IgE syndrome. Authors: Götzberger M, Schlesinger A, Dauer M, Heldwein W, Jansson A, Renner E, Belohradsky BH Journal: Gut Importance of life-long continuous antimicrobial prophylaxis to prevent infections in patients with Job's syndrome. Authors: Agarwal R, Tullu MS, Lahiri KR Journal: Arch Med Res Abnormal expression of CD54 in mixed reactions of mononuclear cells from hyper-IgE syndrome patients. Authors: Martínez AM, Montoya CJ, Rugeles MT, Franco JL, Patiño PJ Journal: Mem Inst Oswaldo Cruz Job's syndrome. Authors: Levin S Journal: S Afr Med J The genetic background of tumour necrosis factor receptor-associated periodic syndrome and other systemic autoinflammatory disorders. Authors: Stjernberg-Salmela S, Ranki A, Karenko L, Pettersson T Journal: Scand J Rheumatol Giant chalazia in the hyperimmunoglobulinemia E (hyper-IgE) syndrome. Authors: Crama N, Toolens AM, van der Meer JW, Cruysberg JR Journal: Eur J Ophthalmol The hyperimmunoglobulin E syndrome. Authors: Hsu CT, Lin YT, Yang YH, Chiang BL Journal: J Microbiol Immunol Infect The development of pulmonary adenocarcinoma in a patient with Job's syndrome, a rare immunodeficiency condition. Authors: Oztop I, Demirkan B, Tarhan O, Kayahan H, Yilmaz U, Kargi A, Alakavuklar M Journal: Tumori Cow's milk allergy in a patient with hyper-IgE syndrome. Authors: Hernandez-Trujillo VP, Nguyen WT, Belleau JT, Jeng M, Conley ME, Lew DB Journal: Ann Allergy Asthma Immunol Mycoplasma pneumatoceles. Authors: Andronikou S, Eimany A, Robinson PJ, Kemp A Journal: S Afr Med J A patient with hyper-IgD syndrome in Antalya, Turkey. Authors: Coban E, Terzio?lu E Journal: Clin Rheumatol Tuberculous brain abscess in a patient with hyper IgE syndrome. Authors: Metin A, Uysal G, Güven A, Unlu A, Oztürk MH Journal: Pediatr Int A man with distinctive facial features and recurrent pyoderma, pneumonia, and skeletal fractures. Authors: Tock CL, Holland SM, Puck JM, Turner ML Journal: J Am Acad Dermatol [Erosive mucosal lichen associated to hyper IgE syndrome and coeliac disease] Authors: Ruiz Villaverde R, Blasco Melguizo J, Menéndez García Estrada A, Díez García F Journal: An Pediatr (Barc) Pulmonary complications of primary immunodeficiencies. Authors: Buckley RH Journal: Paediatr Respir Rev Job's syndrome--a case report. Authors: Verma S, Wollina U Journal: J Eur Acad Dermatol Venereol What made Hanno Buddenbrook sick? Authors: Fischer H Journal: N Engl J Med Autosomal recessive hyperimmunoglobulin E syndrome: a distinct disease entity. Authors: Renner ED, Puck JM, Holland SM, Schmitt M, Weiss M, Frosch M, Bergmann M, Davis J, Belohradsky BH, Grimbacher B Journal: J Pediatr Disseminated pulmonary candidiasis complicating hyperimmunoglobulin E (Job's) syndrome. Authors: Yilmaz E Journal: J Thorac Imaging Keratoconus associated with hyperimmunoglobulin E syndrome. Authors: Kim J, Netto MV Journal: Cornea Extensive xanthelasma associated with anaplastic large cell lymphoma and hyperimmunoglobulin E syndrome. Authors: Lee MW, Choi JH, Sung KJ, Moon KC, Koh JK Journal: Int J Dermatol Eosinophilia and hyperimmunoglobulinemia E as the presenting manifestations of Wegener's granulomatosis. Authors: Kamali S, Kasapoglu E, Aktürk F, Gül A, Inanc M, Ocal L, Aral O, Konice M Journal: Clin Rheumatol [28-Year-Old Patient with Elevated Serum IgE Levels and Multiple Refractory Epidural and Paravertebral Abscesses. Clinical manifestation of a Job's Syndrome?] Authors: Plikat K, Glück T, Völk M, Schölmerich J Journal: Med Klin (Munich) [Images in medicine. Job's Syndrome] Authors: Malbrán A, Rey G, Yeyati EL Journal: Medicina (B Aires) Erythromycin ototoxicity. Authors: McGhan LJ, Merchant SN Journal: Otol Neurotol A 12-year-old girl with asthma, pneumonia, and pneumatoceles. Authors: Tahzib MN, Schuval SJ Journal: Ann Allergy Asthma Immunol Recurrent eosinophilic cystitis with peripheral eosinophilia and hyperimmunoglobulinemia E. Authors: Matsuura H, Sakurai M, Arima K Journal: Urol Int

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